Congenital Pulmonary Vein Stenosis

Volume 1, Jul 2012

S R Mittal, MD, DM, Ajmer, Rajasthan, India

Congenital pulmonary vein stenosis may occur as focal stenosis at the point of entry into left atrium or as generalized hypoplasia of pulmonary vein as in this patient. Pathology may involve one or more pulmonary veins. It is almost always associated with congenital cardiac defects eg:- VSD, ASD, TOF, Tricuspid or Mitral atresia or A-V septal defects. Stenosis of multiple pulmonary veins produces pulmonary venous congestion with dyspnoea, cough & hemoptysis. Secondary pulmonary artery hypertension is a consequence.  


Volume 1, Number 3, e1